J. Brandel, N. Delasnerie-lauprêtre, J. Laplanche, J. Hauw, and A. Alpérovitch, Diagnosis of Creutzfeldt-Jakob disease: Effect of clinical criteria on incidence estimates, Neurology, vol.54, issue.5, pp.1095-1104, 2000.
DOI : 10.1212/WNL.54.5.1095

I. Zerr, K. Kallenberg, D. Summers, C. Romero, A. Taratuto et al., Updated clinical diagnostic criteria for sporadic Creutzfeldt-Jakob disease, Brain, vol.132, issue.10, pp.2659-68, 2009.
DOI : 10.1093/brain/awp191

URL : https://academic.oup.com/brain/article-pdf/132/10/2659/945650/awp191.pdf

P. Burkhard, J. Sanchez, T. Landis, and D. Hochstrasser, CSF detection of the 14-3-3 protein in unselected patients with dementia, Neurology, vol.56, issue.11, pp.1528-1561, 2001.
DOI : 10.1212/WNL.56.11.1528

N. Chitravas, R. Jung, D. Kofskey, J. Blevins, P. Gambetti et al., Treatable neurological disorders misdiagnosed as Creutzfeldt-Jakob disease, Annals of Neurology, vol.256, issue.suppl 1, pp.437-481, 2011.
DOI : 10.1007/s00415-009-5038-1

URL : https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3170496/pdf

J. Laplanche, N. Delasnerie-lauprêtre, J. Brandel, J. Chatelain, P. Beaudry et al., Molecular genetics of prion diseases in France, Neurology, vol.44, issue.12, pp.2347-51, 1994.
DOI : 10.1212/WNL.44.12.2347

A. Alpérovitch, I. Zerr, M. Pocchiari, E. Mitrova, J. De-pedro-cuesta et al., Codon 129 prion protein genotype and sporadic Creutzfeldt-Jakob disease, The Lancet, vol.353, issue.9165, pp.1673-1677, 1999.
DOI : 10.1016/S0140-6736(99)01342-2

N. Privat, V. Sazdovitch, D. Seilhean, J. Laplanche, and J. Hauw, PrP immunohistochemistry: Different protocols, including a procedure for long formalin fixation, and a proposed schematic classification for deposits in sporadic Creutzfeldt-Jakob disease, 1<26::AID- JEMT5>3.0.CO;2-S PMID, pp.26-311097, 2000.
DOI : 10.1016/S0140-6736(96)91412-9

J. Hauw, V. Sazdovitch, J. Laplanche, K. Peoc-'h, N. Kopp et al., Neuropathologic variants of sporadic Creutzfeldt-Jakob disease and codon 129 of PrP gene, Neurology, vol.54, issue.8, pp.1641-1647, 2000.
DOI : 10.1212/WNL.54.8.1641

E. Levavasseur, I. Laffont-proust, E. Morain, B. Faucheux, N. Privat et al., Regulating Factors of PrPres Glycosylation in Creutzfeldt-Jakob Disease - Implications for the Dissemination and the Diagnosis of Human Prion Strains, PLoS ONE, vol.349, issue.7, pp.2786-18665216, 2008.
DOI : 10.1371/journal.pone.0002786.s003

N. Privat, I. Laffont-proust, B. Faucheux, V. Sazdovitch, Y. Frobert et al., Human prion diseases: from antibody screening to a standardized fast immunodiagnosis using automation, Modern Pathology, vol.411, issue.2, pp.140-149, 2008.
DOI : 10.1212/WNL.54.8.1641

J. Brandel, L. Peckeu, and S. Haïk, The French surveillance network of Creutzfeldt???Jakob disease. Epidemiological data in France and worldwide, Transfusion Clinique et Biologique, vol.20, issue.4, pp.395-402, 2013.
DOI : 10.1016/j.tracli.2013.02.029

G. Klug, H. Wand, M. Simpson, A. Boyd, M. Law et al., Intensity of human prion disease surveillance predicts observed disease incidence, Journal of Neurology, Neurosurgery & Psychiatry, vol.5, issue.(RR-13), pp.1372-1379, 2013.
DOI : 10.1071/SH07081

L. Court and J. Hauw, Le docteur Francoise Cathala Pagesy et l???histoire des maladies ?? prions, Revue Neurologique, vol.171, issue.12, pp.805-816, 2015.
DOI : 10.1016/j.neurol.2014.02.003

J. De-pedro-cuesta, M. Glatzel, J. Almazán, K. Stoeck, V. Mellina et al., Human transmissible spongiform encephalopathies in eleven countries: diagnostic pattern across time, 1993???2002, BMC Public Health, vol.353, issue.1, pp.278-17096829, 1993.
DOI : 10.1016/S0140-6736(99)01342-2

URL : https://hal.archives-ouvertes.fr/inserm-00122097

G. Zanusso, M. Fiorini, A. Farinazzo, M. Gelati, M. Benedetti et al., Phosphorylated 14-3-3?? protein in the CSF of neuroleptic-treated patients, Neurology, vol.64, issue.9, pp.1618-1638, 2005.
DOI : 10.1212/01.WNL.0000160397.81314.84

B. Van-everbroeck, I. Dobbeleir, D. Waele, M. , D. Deyn et al., Differential diagnosis of 201 possible Creutzfeldt-Jakob disease patients, Journal of Neurology, vol.251, issue.3, pp.298-304, 2004.
DOI : 10.1007/s00415-004-0311-9

U. Heinemann, A. Krasnianski, B. Meissner, D. Varges, K. Kallenberg et al., Creutzfeldt-Jakob disease in Germany: a prospective 12-year surveillance, Brain, vol.130, issue.5, pp.1350-1359, 2007.
DOI : 10.1093/brain/awm063

E. Gelpi, H. Heinzl, R. Hoftberger, U. Unterberger, T. Strobel et al., Creutzfeldt-Jakob Disease in Austria: An Autopsy-Controlled Study, Neuroepidemiology, vol.30, issue.4, pp.215-236, 2008.
DOI : 10.1159/000126915

C. Jansen, P. Parchi, S. Capellari, C. Ibrahim-verbaas, M. Schuur et al., Human prion diseases in the Netherlands): clinical, genetic and molecular aspects, PLoS One, vol.7, issue.4, p.22558438, 1998.

J. Barash, J. West, A. Demaria, and . Jr, Accuracy of administrative diagnostic data for pathologically confirmed cases of Creutzfeldt-Jakob disease in Massachusetts, 2000-2008, American Journal of Infection Control, vol.42, issue.6, pp.659-64, 2000.
DOI : 10.1016/j.ajic.2014.02.002

R. Paterson, C. Torres-chae, A. Kuo, T. Ando, E. Nguyen et al., Differential Diagnosis of Jakob-Creutzfeldt Disease, Archives of Neurology, vol.69, issue.12, pp.1578-82, 2012.
DOI : 10.1001/2013.jamaneurol.79

I. Nozaki, T. Hamaguchi, N. Sanjo, M. Noguchi-shinohara, K. Sakai et al., Prospective 10-year surveillance of human prion diseases in Japan, Brain, vol.133, issue.10, pp.3043-57, 2010.
DOI : 10.1093/brain/awq216

C. Begué, H. Martinetto, M. Schultz, E. Rojas, C. Romero et al., Creutzfeldt-Jakob Disease Surveillance in Argentina, 1997???2008, Neuroepidemiology, vol.37, issue.3-4, pp.193-202, 1997.
DOI : 10.1159/000331907

C. Gao, Q. Shi, C. Tian, C. Chen, J. Han et al., The epidemiological, clinical, and laboratory features of sporadic Creutzfeldt-Jakob disease patients in China: surveillance data from, PLoS One, vol.6, issue.8, p.21904617, 2006.

S. Soomro and C. Mohan, Biomarkers for sporadic Creutzfeldt-Jakob disease, Annals of Clinical and Translational Neurology, vol.10, issue.Suppl. B, pp.465-72, 2016.
DOI : 10.1038/nnano.2014.254

URL : http://onlinelibrary.wiley.com/doi/10.1002/acn3.304/pdf

R. Atarashi, K. Satoh, K. Sano, T. Fuse, N. Yamaguchi et al., Ultrasensitive human prion detection in cerebrospinal fluid by real-time quaking-induced conversion, Nature Medicine, vol.90, issue.2, pp.175-183, 2011.
DOI : 10.1038/labinvest.2009.68

L. Mcguire, A. Peden, C. Orrú, J. Wilham, N. Appleford et al., Real time quaking-induced conversion analysis of cerebrospinal fluid in sporadic Creutzfeldt-Jakob disease, Annals of Neurology, vol.2, issue.2, pp.278-85, 2012.
DOI : 10.1128/mBio.00078-11

L. Mcguire, A. Poleggi, I. Poggiolini, S. Suardi, K. Grznarova et al., Cerebrospinal fluid real-time quaking-induced conversion is a robust and reliable test for sporadic creutzfeldt-jakob disease: An international study, Annals of Neurology, vol.51, issue.1, pp.160-165, 2016.
DOI : 10.1007/s12035-014-8709-6

G. Zanusso, S. Monaco, M. Pocchiari, and B. Caughey, Advanced tests for early and accurate diagnosis of Creutzfeldt???Jakob disease, Nature Reviews Neurology, vol.37, issue.6, pp.325-358, 2016.
DOI : 10.1038/nprot.2012.067